Title

Journal

Author

WG/TF/Collaboration

IPNA clinical practice recommendations for the diagnosis and management of children with steroid-resistant nephrotic syndrome

Pediatr Nephrol 2020; 35: 1529-1561 

A.Trautmann et al.

Hereditary Glomerulopathies
IPNA

Genetic aspects of congenital nephrotic syndrome: a consensus statement from the ERKNet–ESPN inherited glomerulopathy working group

European Journal of Human Genetics 2020

B. Lipska-Zietkiewicz et al.

Hereditary Glomerulopathies
ESPN

Management of congenital nephrotic syndrome: consensus recommendations of the ERKNet-ESPN Working Group

Nature Reviews Nephrology 2021; 17

O.Boyer et al.

Hereditary Glomerulopathies

ESPN

Clinical practice recommendations for recurrence of focal and segmental glomerulosclerosis/steroid-resistant nephrotic syndrome

Pediatr Transplant

. 2021 May;25(3):e13955.

L. Weber et al.

Pediatric Tx

CERTAIN

Distal renal tubular acidosis: ERKNet/ESPN clinical practice points

Nephrol Dial Transplant 2021; 36: 1585–1596

F. Trepiccione et al.

Tubulopathy

ESPN

Cystinuria : clinical practice recommendation

Kidney International 2021; 99: 48–58

A.Servais et al.

Metabolic and Stone Disorders

Genetic testing in the diagnosis of chronic kidney disease: recommendations for clinical practice

Nephrol Dial Transplant. 2022;
37: 239–254.

N.Knoers et al.

TF Molecular Diagnostics

Definition, diagnosis and clinical management of non-obstructive kidney dysplasia: a consensus statement by the ERKNet Working Group on Kidney Malformations

Nephrol Dial Transplant 2022: 0: 1–12

S.Kohl et al.

CAKUT and obstructive nephropathies

Definition, diagnosis and management of fetal lower urinary tract obstruction

Nat Rev Urol. 2022 Feb 8

V. Capone et al.

CAKUT and obstructive nephropathies

An update on the use of tolvaptan for autosomal dominant polycystic kidney disease: consensus statement on behalf of the ERA Working Group on Inherited Kidney Disorders, the European Rare Kidney Disease Reference Network and Polycystic Kidney Disease International

Nephrol Dial Transplant (2022) 37: 825–839

R. Müller et al

AD structural kidney disorders

ERA

Clinical practice recommendations for primary hyperoxaluria: an expert consensus statement from ERKNet and OxalEurope

Nature Reviews Nephrology  2023 ;
19 : 194–211

J.W.Groothoff et al.

Metabolic and Stone Disorders

Oxaleurope

D. Reijman et al.

Pediatric CKD/Dialysis

ESPN

Clinical practice recommendations for kidney involvement in tuberous sclerosis complex: a consensus statement by the ERKNet Working Group for Autosomal Dominant Structural Kidney Disorders and the ERA Genes & Kidney Working Group

Nature Reviews Nephrology 2024

D. Mekahli et al.

AD structural kidney disorders

ERA

Topic

Working Group

Collaboration

Status

 Nephrogenic diabetic insipidus

Metabolic Nephropathies

In Revision (NRN)

 Bardet Biedl 

AD Structural Disorders

ERN-Eye

In Revision

 Methylmalonic aciduria

Metabolic Nephropathies

In Revision (KI)

 Cardiovascular evaluation and management in ped CKD

PedCKD&Dialysis

ESPN

Paper in final preparation

 Attenuation of CKD progression

PedCKD&Dialysis

ESPN

Paper in preparation

 Spinal Dysraphism

CAKUT and Ciliopathies

eUROGEN

Delphi Survey

First f2f meeting held on 21/22 June 2024

 Monoclonal gammopathies of renal significance

Immune glomerulopathies

EuroBloodNet

First draft ready – in review

 Lowe Syndrome

 Metabolic nephropathies

Writing draft recommendations

 Hypomagnesemia

Tubulopathies

ERA

Literature screening

 Megaureter

 CAKUT and Ciliopathies

eUROGEN

Literature screening

Postnatal PUV

CAKUT/Ciliopathies

eUROGEN

In planning

Nephrocalcinosis

Tubulopathies

In Planning

VUR

CAKUT/Ciliopathies

In planning

Topic

Working Group

Collaboration

Status

Postnatal PUV

CAKUT/Ciliopathies

eUROGEN

In planning

Nephrocalcinosis

Tubulopathies

In Planning

VUR

CAKUT/Ciliopathies

In planning