Overview ERKNet Guideline Projects
Updated 12 May 2025
Please find below the overview of all published, ongoing and planned guidelines
Title | Journal | Author | WG/TF/Collaboration |
|---|---|---|---|
| Diagnosis, management and treatment of the Alport syndrome | Nephrol Dial Transplant 2025 | Torra et al. | Hereditary Glomerulopathies ERA ESPN |
| Diagnosis and management of spinal dysraphism in children and adolescents | EAU Guidelines Office 2025 | K. Abrahamson et al. | eUROGEN ERN-ITHACA EAU ESPU |
| Dent disease: Clinical Practice Recommendations | Nephrol Dial Transplant 2025 | D. Bökenkamp et al. | Metabolic Nephropathies Tubulopathies ESPN |
| International Expert Consensus Statement on the Diagnosis and Management of Congenital Nephrogenic Diabetes Insipidus (arginine vasopressin resistance) | Nature Review Nephrology 2024 | E. Levtchenko et al. | Tubulopathies ESPN |
| Clinical Practice Recommendations on Kidney Management in Methylmalonic Acidemia: an Expert Consensus Statement From ERKNet and MetabERN | Kidney International Reports 2024 | A. Servais et al. | Metabolic and Stone Disorders, Tubulopathies Metab-ERN |
| Clinical practice recommendations for kidney involvement in tuberous sclerosis complex: a consensus statement by the ERKNet Working Group for Autosomal Dominant Structural Kidney Disorders and the ERA Genes & Kidney Working Group | Nature Reviews Nephrology 2024 | D. Mekahli et al. | AD structural kidney disorders ERA |
| Atherosclerosis, Volume 392, May 2024, 117525 | D. Reijman et al. | Pediatric CKD/Dialysis ESPN |
| Nature Reviews Nephrology 2023 ;
| J.W.Groothoff et al. | Metabolic and Stone Disorders Oxaleurope |
| An update on the use of tolvaptan for autosomal dominant polycystic kidney disease: consensus statement on behalf of the ERA Working Group on Inherited Kidney Disorders, the European Rare Kidney Disease Reference Network and Polycystic Kidney Disease International | Nephrol Dial Transplant (2022) 37: 825–839 | R. Müller et al | AD structural kidney disorders ERA |
| Definition, diagnosis and management of fetal lower urinary tract obstruction | Nat Rev Urol. 2022 Feb 8 | V. Capone et al. | CAKUT and obstructive nephropathies |
| Nephrol Dial Transplant 2022: 0: 1–12
| S.Kohl et al. | CAKUT and obstructive nephropathies |
Genetic testing in the diagnosis of chronic kidney disease: recommendations for clinical practice
| Nephrol Dial Transplant. 2022; 37: 239–254. | N.Knoers et al. | TF Molecular Diagnostics |
| Cystinuria : clinical practice recommendation | Kidney International 2021; 99: 48–58
| A.Servais et al. | Metabolic and Stone Disorders |
Distal renal tubular acidosis: ERKNet/ESPN clinical practice points
| Nephrol Dial Transplant 2021; 36: 1585–1596
| F. Trepiccione et al. | Tubulopathy ESPN |
| Pediatr Transplant . 2021 May;25(3):e13955. | L. Weber et al. | Pediatric Tx CERTAIN |
| Nature Reviews Nephrology 2021; 17
| O.Boyer et al. | Hereditary Glomerulopathies ESPN |
| Genetic aspects of congenital nephrotic syndrome: a consensus statement from the ERKNet–ESPN inherited glomerulopathy working group | European Journal of Human Genetics 2020 | B. Lipska-Zietkiewicz et al. | Hereditary Glomerulopathies ESPN |
| Topic | Working Group | Collaboration | Status |
| Cardiovascular evaluation and management in ped CKD | PedCKD&Dialysis | ESPN | Paper in final preparation |
| Attenuation of CKD progression | PedCKD&Dialysis | ESPN | Paper in preparation |
| ARPKD | CAKUT and Ciliopathies | ESPN | Delphi Round |
| Monoclonal gammopathies of renal significance | Immune glomerulopathies | EuroBloodNet | Paper in preparation |
| Lowe Syndrome | Metabolic nephropathies | Writing draft recommendations | |
| William Beuren Syndrome | CAKUT and Ciliopathies | ERN-ITHACA | Writing draft recommendation |
| cTTP | TMA | Writing draft recommendation | |
| Hypomagnesemia | Tubulopathies | ERA | Literature screening |
| Megaureter | CAKUT and Ciliopathies | eUROGEN | Literature screening |
| Nephrocalcinosis | Tubulopathies | Literature screening | |
| KRT | Pediatric CKD/Dialysis | Litrature screenining | |
| Postnatal PUV | CAKUT/Ciliopathies | eUROGEN | In planning |
| VUR | CAKUT/Ciliopathies | In planning for 2025 |
update 20.11.2014
Topic | Working Group | Collaboration | Status |
Postnatal PUV | CAKUT/Ciliopathies | eUROGEN | In planning |
VUR | CAKUT/Ciliopathies |
| In planning |